Sellar and Stalk Region Histiocytosis: Report of Two Adolescent Cases and Management Challenges

Abstract

Background: Histiocytosis is relatively rare disease which may be focal or with multiorgan involvement and in many cases with unpredictable course.

Case presentation: We report two cases of adolescent histiocytosis; one with multiorgan involvement and sellar region tumor and a case with isolated sellar and suparasellar histiocytosis and discuss challenges that must be overcome.

Conclusion: Sellar histiocytosis is a challenge to manage and surgery may have a role to decompress optic apparatus and confirm diagnosis. Immunohistochemical study is very helpful to diagnose this type of tumor.

 Keywords: Histiocytosis, Sellar tumor, Pituitary tumor, Pituitary stalk tumor