Rare histological subtype of pulmonary artery intimal sarcoma diagnosed by multidisciplinary approach

Abstract

Pulmonary artery intimal sarcoma (PAS) is a rare mesenchymal tumor mostly diagnosed in middle?aged women. In a 63?year?old female, the radiological fndings showed cavitation in the left upper lobe of the lung and infltrative tumor mass around the left pulmonary artery. PAS consisted of small, round tumor cells with about 80% of mitotic activity and with myxoid background and specifc immunoprofle and diagnosed as undi?erentiated sarcoma with round cell features type. Te fnal diagnosis of PAS was established according to the pathohistological, chest computed tomography scan, and surgery fnding.